IDH2

Oncogene
Isocitrate dehydrogenase [NADP], mitochondrial UniProt accession P48735

Plays a role in intermediary metabolism and energy production (PubMed:19228619, PubMed:22416140). It may tightly associate or interact with the pyruvate dehydrogenase complex (PubMed:19228619, PubMed:22416140)

Source: UniProt

Homodimer

Source: UniProt
Mitochondrion
Source: UniProt
  • D-2-hydroxyglutaric aciduria 2 (D2HGA2)

    A neurometabolic disorder causing developmental delay, epilepsy, hypotonia, and dysmorphic features. Both a mild and a severe phenotype exist. The severe phenotype is homogeneous and is characterized by early infantile-onset epileptic encephalopathy and cardiomyopathy.

    The mild phenotype has a more variable clinical presentation. Diagnosis is based on the presence of an excess of D-2-hydroxyglutaric acid in the urine.

  • Glioma (GLM)

    Gliomas are benign or malignant central nervous system neoplasms derived from glial cells. They comprise astrocytomas and glioblastoma multiforme that are derived from astrocytes, oligodendrogliomas derived from oligodendrocytes and ependymomas derived from ependymocytes.

  • Unknown disease
Source: UniProt

Click a pathway to open the interactive Reactome viewer.

Pathway list and interactive viewer: Reactome

Synthetic Lethal Network

Genes with an experimentally identified or computationally predicted synthetic-lethal relationship to IDH2, aggregated across our SSL data sources. Click any partner node to view that gene’s page.

Nodes and edges are coloured by the SSL data source. Partners appearing in more than one source are shown in grey.

BioGRID SLOrth SynLethDB MexDrugs Multi-source
Sources: BioGRID, SLOrth, SynLethDB, MexDrugs

Clinical Trials

Total Trials Found: 59

NCT ID Condition Brief Title Phase Status
NCT03383575 Acute Myeloid Leukemia, Blasts 20-30 Percent of Bone Marrow Nucleated Cells, Chronic Myelomonocytic Leukemia, IDH2 Gene Mutation, Myelodysplastic Syndrome With Excess Blasts, Recurrent High Risk Myelodysplastic Syndrome, Refractory High Risk Myelodysplastic Syndrome Azacitidine and Enasidenib in Treating Patients With IDH2-Mutant Myelodysplastic Syndrome PHASE2 RECRUITING
NCT04203316 Recurrent Acute Myeloid Leukemia, Refractory Acute Myeloid Leukemia Enasidenib for the Treatment of Relapsed or Refractory Acute Myeloid Leukemia Patients With an IDH2 Mutation PHASE2 ACTIVE_NOT_RECRUITING
NCT03878095 Malignant Solid Neoplasm, Refractory Cholangiocarcinoma, Refractory Malignant Solid Neoplasm Testing Olaparib and AZD6738 in IDH1 and IDH2 Mutant Tumors PHASE2 ACTIVE_NOT_RECRUITING
NCT03914742 IDH1 Mutation, IDH2 Mutation, Recurrent Glioblastoma, Recurrent WHO Grade II Glioma, Recurrent WHO Grade III Glioma BGB-290 and Temozolomide in Treating Patients With Recurrent Gliomas With IDH1/2 Mutations PHASE1, PHASE2 COMPLETED
NCT06387069 Acute Myeloid Leukemia A Study to Evaluate HMPL-306 in Patients With IDH1or IDH2-mutated Acute Myeloid Leukemia PHASE3 RECRUITING
NCT04603001 Acute Myeloid Leukemia (AML), Myelodysplastic Syndrome (MDS), Chronic Myelomonocytic Leukemia (CMML), Myeloproliferative Neoplasms (MPNs) Study of Oral LY3410738 in Patients With Advanced Hematologic Malignancies With IDH1 or IDH2 Mutations PHASE1 ACTIVE_NOT_RECRUITING
NCT03204838 Acute Myeloid Leukemia (AML) IDH1/IDH2 Mutation Frequency in Acute Myeloblastic Patients N/A UNKNOWN
NCT03515512 Acute Myeloid Leukemia, Chronic Myelomonocytic Leukemia IDH2 Inhibition Using Enasidenib as Maintenance Therapy for IDH2-mutant Myeloid Neoplasms Following Allogeneic Stem Cell Transplantation PHASE1 COMPLETED
NCT07448480 Recurrent Malignant Glioma, Glioblastoma, Anaplastic Astrocytoma, Pleomorphic Xanthoastrocytoma Comprehensive Analysis of Chemotherapy and Targeted Therapy Outcomes in Recurrent Malignant Gliomas N/A ACTIVE_NOT_RECRUITING
NCT05592743 Glioma, Recurrence, Disease Attributes, Pathologic Processes, Neoplasms, Neuroepithelial, Neuroectodermal Tumors, Neoplasms, Germ Cell and Embryonal, Neoplasms by Histologic Type, Neoplasms, Neoplasms, Glandular and Epithelial, Neoplasms, Nerve Tissue Vorasidenib Expanded Access Program N/A APPROVED_FOR_MARKETING