DBH

Dopamine beta-hydroxylase UniProt accession P09172

Catalyzes the hydroxylation of dopamine to noradrenaline (also known as norepinephrine), and is thus vital for regulation of these neurotransmitters

Source: UniProt

Homotetramer; composed of two disulfide-linked dimers

Source: UniProt
Cytoplasmic vesicle, secretory vesicle lumen, Cytoplasmic vesicle, secretory vesicle, chromaffin granule lumen, Secreted Cytoplasmic vesicle, secretory vesicle membrane — Single-pass type II membrane protein, Cytoplasmic vesicle, secretory vesicle, chromaffin granule membrane — Single-pass type II membrane protein
Source: UniProt
  • Orthostatic hypotension 1 (ORTHYP1)

    A form of orthostatic hypotension due to congenital dopamine beta-hydroxylase deficiency. Orthostatic hypotension, also known as postural hypotension, is a finding defined as a 20-mm Hg decrease in systolic pressure or a 10-mm Hg decrease in diastolic pressure occurring 3 minutes after a person has risen from supine to standing. Symptoms include dizziness, blurred vision, and sometimes syncope.

    ORTHYP1 is an autosomal recessive condition apparent from infancy or early childhood and characterized by low plasma and urinary levels of norepinephrine and epinephrine, and episodic hypoglycemia.

Source: UniProt

Click a pathway to open the interactive Reactome viewer.

Pathway list and interactive viewer: Reactome

Synthetic Lethal Network

Genes with an experimentally identified or computationally predicted synthetic-lethal relationship to DBH, aggregated across our SSL data sources. Click any partner node to view that gene’s page.

Nodes and edges are coloured by the SSL data source. Partners appearing in more than one source are shown in grey.

BioGRID SLOrth SynLethDB MexDrugs Multi-source
Sources: BioGRID, SLOrth, SynLethDB, MexDrugs

Clinical Trials

Total Trials Found: 315

NCT ID Condition Brief Title Phase Status
NCT01927055 Symptomatic Neurogenic Orthostatic Hypotension, Parkinson's Disease, Multiple Systems Atrophy, Pure Autonomic Failure, Dopamine Beta Hydroxylase Deficiency A Clinical Study of Patients With Symptomatic NOH to Assess Sustained Effects of Droxidopa Therapy PHASE3 TERMINATED
NCT00581477 Autonomic Nervous System Diseases, Orthostatic Hypotension, Dopamine Beta-Hydroxylase Deficiency, Orthostatic Intolerance Treatment of Orthostatic Hypotension PHASE2, PHASE3 TERMINATED
NCT00659230 Posttraumatic Stress Disorder Nepicastat for Posttraumatic Stress Disorder (PTSD) in OIF/OEF Veterans PHASE2 COMPLETED
NCT02586623 Symptomatic Neurogenic Orthostatic Hypotension Sustained Effect of Droxidopa in Symptomatic Neurogenic Orthostatic Hypotension PHASE4 COMPLETED
NCT01828489 Pediatric Acute Myeloblastic Leukemia Research Study for Treatment of Children and Adolescents With Acute Myeloid Leukaemia 0-18 Years PHASE3 UNKNOWN
NCT00395850 Cocaine Dependence Disulfiram for Cocaine Abuse PHASE2 COMPLETED
NCT00782340 Symptomatic Neurogenic Orthostatic Hypotension (NOH), Non-diabetic Neuropathy, Primary Autonomic Failure, Dopamine Beta Hydroxylase Deficiency A Clinical Study for Patients With Neurogenic Orthostatic Hypotension (NOH) Using Droxidopa PHASE3 COMPLETED
NCT00149630 Cocaine Dependence, Opioid Dependence Pharmacogenetics of Disulfiram for Cocaine PHASE2 COMPLETED
NCT00889135 Dopamine Beta Hydroxylase (DBH) Deficiency Long Term Treatment With L-DOPS N/A APPROVED_FOR_MARKETING
NCT00913484 Cocaine Dependence, Opioid Dependency Disulfiram for Cocaine Abuse in Buprenorphine Treatment PHASE2 COMPLETED